Double outlet right ventricle
Double outlet right ventricle is a form of congenital heart disease where both of the great arteries connect to the right ventricle. In some cases it is found that this occurs on the left side of the heart rather than the right side.Pathogenesis
DORV occurs in multiple forms, with variability of great artery position and size, as well as of ventricular septal defect location. It can occur with or without transposition of the great arteries. The clinical manifestations are similarly variable, depending on how the anatomical defects affect the physiology of the heart, in terms of altering the normal flow of blood from the RV and left ventricle to the aorta and pulmonary artery. For example:Treatment
DORV is treated with surgery.Epidemiology
DORV affects between 1% and 3% of people born with congenital heart defects.
Chromosomal abnormalities were reported in about 40% of reported cases in the medical literature.
